Paediatric Imaging

Kartagener's syndrome

(Manes Kartagener 1897 - 1975, Swiss physician), syndrome comprising the association of situs inversus, sinusitis and ciliary dyskinesia. Clinically, the children have sinusitis and bronchiectasis. Radiologically, there is either complete situs inversus or isolated dextrocardia, sinusitis and bronchiectasis (Fig.1). See ciliary dyskinesia

 

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Fig.1

PA chest radiograph of a child with Kartagener's syndrome. Note dextrocardia, basal bronchiectasis and situs inversus. The stomach bubble is on the right.
Kartagener's syndrome, Fig.1