Campanacci's syndrome

(Mario Campanacci, 20th century, Italian physician) (also called Jaffe Campanacci syndrome), the combination of pain, swelling and caf-au-lait spots with variable presence of developmental delay and hypogonadism. Radiologically, there are multiple, non-ossifying fibroma found dominantly in the long bones, pelvis and mandible. There may be kyphoscoliosis.

HC