Cardiovascular Imaging

Cystic medial necrosis

degenerative disease of the media of the aorta and other arteries with loss of elastic tissue and muscle cells. It is a pathological substrate for aortic dissection. It may also be manifested by proximal aortic ectasia or aneurysm. Cystic medial necrosis may occur as an isolated abnormality or as part of a systemic connective tissue disease such as Marfans syndrome or Ehlers Danlos syndrome. There is an increased risk of cystic medial degeneration and aortic or arterial dissection during pregnancy.

CBH