Chest Imaging

Hughes stovin syndrome

(John Patterson Hughes, 20th century, British physician and Peter George Ingle Stovin, 20th century, British physician), a variant of Behcets disease. It is even more rare than Behcet's disease, most patients being young adult males in the second to fourth decades. The major features are:

  • systemic venous thrombi involving the vena cava, cerebral sinuses and limb veins;

  • pulmonary artery occlusions due to emboli or thrombi; and

  • one or more segmental pulmonary artery aneurysms.

    Common clinical presentations include venous thrombosis, fever and haemoptysis. Radiological features are similar to those of Behcets disease (Fig.1).

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    Fig.1

    Contrast-enhanced CT scan of the chest in a patient with thrombosis of the inferior vena cava and Bechet's disease showing bilateral aneurysms of the interlobar pulmonary arteries. Mural thrombosis is present in both aneurysms.
    Hughes stovin syndrome, Fig.1