Musculoskeletal ImagingLymphangiomatosis
multiple intraosseous
lymphangiomas occurring as a
diffuse form as part of a spectrum of either
cystic haemangiomatosis or massive osteolysis (
Gorhams disease). For a general description, see
lymphangiomatosis.
In this disorder, the lymphangiomas may involve two or more widely separated bones, several bones in the same region of the body or many bones in a diffuse pattern; in some cases lymphangiomas also occur in the soft tissues or viscera. Most often the long tubular bones and flat or irregular bones are affected. Lymphangiography is valuable in making a specific diagnosis through uptake of contrast agent in intraosseous tumours.
DR