Musculoskeletal Imaging

Fibromatosis

various types of benign fibrous proliferations of soft tissue unrelated to reparative scar tissue. Two principal groups are distinguished: a congenital or childhood form, and a form usually occurring in adults (Table 1).

Fibromatosis, Table 1. Various types of fibromatoses

DiagnosisSite of involvement
Congenital generalized fibromatosis (infantile myofibromatosis)Soft tissue, viscera, bone
Infantile digital fibromatosisFingers and toes
Fibromatosis colliSternocleidomastoid muscle
Juvenile aponeurotic fibromaHands and feet
Juvenile hyaline fibromatosisDermis and subcutis
Infantile desmoid type fibromatosisMusculature
Palmar fibromatosisHands
Plantar fibromatosisFeet
Peyronie's diseasePenis
Abdominal or extraabdominal fibromatosis (desmoid tumours)Musculature
Intraabdominal fibromatosis (pelvic fibromatosis, Gardners syndromeMusculature, mesentery

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