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Myxopapillary ependymoma grade I (WHO)

 

Clinical history
For one year, this 36-year-old male presented mainly with chronic low back pain with some painful radiation to the left leg. Recently, he complained of bowel and bladder dysfunction and impotence.

Neurological examination
Hypoesthesia of the lateral left leg was observed with hyperreflexia, without motor deficit.

MRI findings
Image 1: Sagittal T1WI: L1-L2 solid tumor isointense to cord with a caudal cyst pushing the conus upwards.
Image 2: Sagittal T2WI: The solid nodule shows heterogeneous low signal intensity with well defined contours. The associated cyst is hyperintense. Posterior and upwards displacement of the conus is best demonstrated.
Image 3: Sagittal Gd T1WI: The tumor enhances intensely although heterogeneously following contrast administration.
Image 4: Axial GD T1WI and image 5: Coronal GD T1WI. The tumor entirely fills the spinal canal. The tumor-associated cyst has non enhancing borders.

Surgery
Total resection of a well delineated non infiltrating filum terminale tumor.

Clinical follow-up
The patient recovered progressively and became free of symptoms.

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Fig. 1

Myxopapillary ependymoma grade I (WHO), Fig. 1
Myxopapillary ependymoma grade I (WHO), Fig. 2
Myxopapillary ependymoma grade I (WHO), Fig. 3
Myxopapillary ependymoma grade I (WHO), Fig. 4
Myxopapillary ependymoma grade I (WHO), Fig. 5